Searchable abstracts of presentations at key conferences in endocrinology

ea0029p54 | Adrenal cortex | ICEECE2012

Frequency and causes of adrenal crises over life-time in patients with 21-hydroxylase deficiency

Reisch N. , Willige M. , Kohn D. , Schwarz H. , Allolio B. , Reincke M. , Quinkler M. , Hahner S. , Beuschlein F.

Background: Adrenal crisis (AC) is a life-threatening complication in patients with congenital adrenal hyperplasia due to classical 21-hydroxylase deficiency (21-OHD). AC was defined as an acute state of health impairment which required i.v. glucocorticoid administration and hospital admission. No data on AC over life-time in 21-OHD is available.Study design: In a retrospective study AC was studied following two approaches: a) questionnaire-based: 122 ad...